1;Foreword;4 2;Preface;5 3;Contents;7 4;List of Contributors;12 5;Hirschsprung's Disease: A Historical Perspective - 1691- 2005;15 6;Development of the Enteric Nervous System;27 7;Functional Anatomy of the Enteric Nervous System;35 8;Animal Models of Aganglionosis;64 9;The Molecular Genetics of Hirschsprung's Disease;76 10;Normal Colonic Motor Function and Relevant Structure;92 11;Pathophysiology of Hirschsprung's Disease;107 12;Hirschsprung's Disease: Clinical Features;119 13;Congenital Anomalies and Genetic Associations in Hirschsprung's Disease;126 14;Enterocolitis Complicating Hirschsprung's Disease;143 15;Diagnosis of Hirschsprung's Disease and Allied Disorders;154 16;Functional Diagnosis;161 17;Histopathological Diagnosis and Differential Diagnosis of Hirschsprung's Disease;193 18;NADPH- Diaphorase Histochemistry;206 19;Immunohistochemical Studies;214 20;Electron Microscopic Studies of Hirschsprung's Disease;228 21;Intestinal Neuronal Malformations ( IND): Clinical Experience and Treatment;236 22;Neurocristopathies and Particular Associations with Hirschsprung's Disease;259 23;Megacystis- Microcolon- Intestinal Hypoperistalsis Syndrome;273 24;Degenerative Hollow Visceral Myopathy Mimicking Hirschsprung's Disease;280 25;Adynamic Bowel Syndrome;292 26;Anal Sphincter Achalasia and Ultrashort Hirschsprung's Disease;302 27;Laparoscopically Assisted Anorectal Pull- Through;328 28;Swenson's Procedure;333 29;Soave's Extramucosal Endorectal Pull- Through Procedure;340 30;Rehbein's Procedure ( Deep Anterior Resection);352 31;Chaptername Transanal Pull- Through for Hirschsprung's Disease;362 32;Duhamel's Procedure;368 33;Early and Late Complications Following Operative Repair of Hirschsprung's Disease;377 34;Long- Term Results and Quality of Life After Treatment of Hirschsprung's Disease and Allied Disorders;388 35;Subject Index;398