This book, built on the latest internationally recognized classification system to which the volume editor contributed, offers a unique and comprehensive reference guide to the clinical presentation, characteristics and proper treatment of the wide spectrum of congenital malformations of the inner ear (IEM). 

IEMs are common, accounting for roughly 20% of congenital hearing loss cases, and can be difficult to manage: 8 groups are identified, which are completely different from each other. With a wealth of color figures and extra videos, the book provides an in-depth description of all the relevant aspects: from histopathology assessment, to preoperative evaluation, genetics, different surgical and non-surgical options, and outcomes. The results from two international Consensus Pediatric Auditory Brainstem Implantation Meetings are also included.

Written by leading experts in the field, this volume will be an invaluable and multidisciplinary tool for otolaryngologists, audiologists and radiologists, while also benefiting scientists dealing with genetics, and neurosurgeons dealing with brainstem implants. 

Section I: general concepts 1. IntroductionClassification

2 Histopathology of IEM. Section II: Preoperative Evaluation: 3 ENT
4 Audiology
5 Radiology
6 Speech and Language Evaluation
7 Psychology.-8 Neurosurgery
9 Genetic evaluation. Section III: IEM management: 10 Genetics of IEM
11 Treatment Algorithm
12 CSF Fistula and meningitis
13 Facial nerve Abnormalities
14 Stapedotomy
15 CSF leakage and management
16 First Consensus Meeting
17 CI vs ABI in IEMs
18 ABI Surgery
19 Complete Labyrinthine Aplasia
20 Rudimentary Otocyst
21 Common Cavity
22 Cochlear Aplasia
23 IP-I
24 IP-II
25 IP-III
26 Cochlear Hypoplasia. -27 EVA ?
28 Cochlear Aperture Abnormalities
29 Cochlear Nerve Deficiency
30 Vestibular Malformations<i>
</i>31 Second Consensus Meeting
32 Audiological Outcome with CI<i>
</i>33<i> </i>Audiological Outcome with ABI.