In recent years new, obscure or poorly known dermatological disorders have been described and better defined, with emphasis on clinical, histopathological and etiopathogenetic features. Familiarity with these new, emerging or revisited clinical entities is fundamental, and recognizing them with their differential diagnosis has important implications in clinical practice for better patient management.

This book offers an in-depth discussion of the clinical and pathologic features of newly described or less well-known and revisited cutaneous disorders. It provides clinical findings, as well as the histologic, immunologic, and molecular features of these diseases in addition to therapeutic notes. The first section of the book covers cutaneous diseases that lack any systemic implications, such as circumscribed palmoplantar hypokeratosis, necrotizing infundibular crystalline folliculitis, and dermal hyperneury, amongst others. The second section offers coverage on cutaneous diseases with systemic implications, such as AESOP-POEMS syndrome, lipoatrophic panniculitis of children, and obesity associated with lymphedematous mucinosis. Each chapter describes an entity, along with an atlas of clinical manifestations that will serve as a "bed-side" clinical reference, followed by a series of photomicrographs depicting the histologic changes. Chapters also offer recent updates on molecular tools helpful in attaining the diagnosis as well as therapeutic recommendations based upon the more recent acquisitions. 

New and Emerging Entities in Dermatology and Dermatopathology  is a must-have reference for the practicing dermatopathologist, internists, general pathologist reviewing skin biopsies, general dermatologists, family practitioners and nurse practitioners, geneticists, immunologists and other health care providers that care for patients with skin conditions.

 

Part 1. ENTITIES WITHOUT OR LITTLE SYSTEMIC IMPLICATIONS

1.Autoinflammatory Keratinization Diseases
2.Adult Mucinoses: New And Revisited Variants
3.Pediatric Cutaneous Mucinoses
4.Circumscribed Palmoplantar Hypokeratosis
5.Necrotizing Infundibular Crystalline Folliculitis And Necrotizing Eosinophilic Folliculitis
6.Annular Erythema: New And Revisited Variants
7.Frontal Fibrosing Alopecia
8.Terra Firma-Forme Dermatosis And Dermatosis Neglecta
9.Papular Epidermal Nevus With "Skyline" Basal Cell Layer (PENS)
10.Grover Disease
11.The Spectrum Of Acquired Elastolytic Disorders
12.Post Irradiation Pseudo-Sclerodermatous Panniculitis
13.Linear Focal Elastosis And Pxe-Like Fibroelastolytic And Elastotic Papulosis Disorders
14. Rare Variants Of Keratosis Pilaris
15.Cutaneous Collagenous Vasculopathy
16.Acquired Hyperpigmentation Disorders Of Uncertain Etiology
17. Eruptive pseudoangiomatosis, eruptive hypomelanosis and paraviral exanthems
18.Morbihan Disease
Part 2.ENTITIES WITH SYSTEMIC IMPLICATIONS
19.Aquagenic Keratoderma
20.New Or Unusual Skin Manifestations In Monoclonal Gammopathies
21.Lipophagic/Lipoatrophic Panniculitis: A Th1 Mediated Autoimmune Disorder Of The Subcutaneous Fat
22.Covid19-Related Cutaneous Manifestations
23.PAPA, PASH, PAPASH, PsAPASH and PASS: autoinflammatory syndromes of Hidradenitis Suppurativa
24.Re-Emerging And New Skin Infections
25.Skin Adverse Reactions From New Cancer Immunotherapy
26.Newly Recognized Variants Of Neutrophilic Dermatosis
27.Cutaneous Reactive Angiomatoses
28.Skin Manifestations of Immunoglobulin G4-Related Disease
29.Necrolytic Acral Erythema (NAE)
30.Reactive Granulomatous Dermatitis (Interstitial granulomatous dermatitis, palisaded neutrophilic and granulomatous dermatitis, and variants)
31.Chronic Atypical Neutrophilic Dermatosis With Lipodystrophy And Elevated Temperature (CANDLE) and Proteasome Associated Autoinflammatory Syndrome (PRAAS)
32.Spiny Keratoderma
33.Cocaine-Levamisole-Induced Vasculitis/Vasculopathy Syndrome
34.Lymphocytic Thrombophilic Arteritis (Macular Lymphocytic Arteritis)
35.Dermal Hyperneury
36.Emergent cutaneous T-cell pseudolymphomas.