Pediatric Bone Marrow

Pediatric Bone Marrow

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in Vorbereitung

No other book covers the pathology of the bone marrow in children as extensively as Pediatric Bone Marrow. It provides a wide background for the understanding of bone marrow disease in children and its difference from that of the adult population. The text illustrates the morphology of the peripheral blood, bone marrow aspirate and bone marrow biopsy. It is useful for the diagnosis of pediatric disorders in the bone marrow, making it an ideal guide for pediatric pathologists, hematologists, oncologists and medical technologists or any physician involved in the diagnosis of pediatric bone marrow disorders.



1 Normal Bone Marrow
References
2 Inherited Bone Marrow Failure
Inherited Hematopoietic Syndromes Associated with Pancytopenia
Fanconi Anemia
Laboratory Findings
Dyskeratosis Congenita
Laboratory Findings
Shwachman-Diamond Syndrome
Laboratory Findings
Congenital Amegakaryocytic Thrombocytopenia
Laboratory Findings
Rare Familial Marrow Failure Syndromes
Inherited Hematopoietic Syndromes Associated with Single Cytopenia
Diamond-Blackfan Anemia
Laboratory Findings
Congenital Dyserythropoietic Anemias
Severe Congenital Neutropenia
Laboratory Findings
Cyclic Neutropenia
Laboratory Findings
Chronic Benign Neutropenia
Thrombocytopenia with Absent Radii
Laboratory Findings
Inherited Disorders of the Leukocytes Associated with Change in their Morphology
Pelger-Hüet Anomaly
May-Hegglin Anomaly
Chédiak-Higashi Syndrome
Alder-Reilly Anomaly
Other Morphological Abnormalities
Inherited Immunodeficiency
Reticular Dysgenesis (Alymphocytic Neutropenia)
Laboratory Findings
X-Linked Agammaglobulinemia (Bruton Agammaglobulinemia)
Laboratory Findings
Cartilage-Hair Hypoplasia
Laboratory Findings
Wiskott-Aldrich Syndrome
Laboratory Findings
Omenn Syndrome
Laboratory Findings
Inherited Sideroblastic Anemias
Laboratory Findings
?-Aminolevulinate Synthase (ALAS2) Deficiency
Pearson Syndrome
Osteopetrosis
Laboratory Findings
References
3 Macrophage- and Dendritic-Cell-Related Disorders Including the Lysosomal Storage Disorders
Storage Disorders
Gaucher Disease
Laboratory Findings
Niemann-Pick Disease
Laboratory Findings
Wolman Disease
Fabry Disease
Sialidoses
Gangliosidosis GM1 and GM2
Fucosidosis
OC-Mannosidosis
Glycogen Storage Diseases
Mucopolysaccharidosis
Cystinosis
Primary Hyperoxaluria
Sea-blue Histiocytosis
Histiocytosis
Langerhans Cell Histiocytosis
Laboratory Findings
Xanthoma Disseminatum
Macrophage-Related Disorders
Hemophagocytic Syndrome
Laboratory Findings
References
4 Bone Marrow Infections
Infection-Associated Hemophagocytic Syndrome
Granulomas
Bacterial Infections
Mycobacteria
Ehrlichiosis
Fungus
Viruses
Human Parvovirus B19
Epstein-Barr-Virus
Cytomegalovirus
Human Immune Deficiency Virus
Human Herpesvirus Type 6
Other Viruses
Parasites
Malaria
Other Parasites
References
5 Bone Marrow Metastases
Laboratory Findings
Neuroblastoma
Laboratory Findings
Rhabdomyosarcoma
Laboratory Findings
wing Family of Tumors
Laboratory Findings
Desmoplastic Small Round-Cell Tumor
Central Nervous System
Laboratory Findings
Other Metastatic Tumors
References
6 Hematologie Manifestations of Trisomy 21
Laboratory Findings
Acute Megakaryoblastic Leukemia (FAB M7)
Laboratory Findings
Cytochemistry and Immunocytochemistry
Electron Microscopy
Cytogenetic and Molecular Genetics
References
7 Myelodysplastic Syndromes
Myelodysplastic and Myeloproliferative Disorders
Myelodysplastic Syndromes
Juvenile Myelomonocytic Leukemia
Laboratory Findings
Monosomy 7 Syndrome
Unclassifiable Myelodysplastic Syndromes
MDSs that Fit the FAB Classification in Children
Laboratory Findings
Myeloproliferative Disorders
Chronic Myelogenous Leukemia
Laboratory Findings
Chronic Neutrophilic Leukemia
Polycythemia Disorders
Polycythemia Vera
Laboratory Findings
Essential Thrombocythemia
Laboratory Findings
Hypereosinophilic Syndrome/ Chronic Eosinophilic Leukemia
Laboratory Findings
Systemic Mastocytosis
Laboratory Findings
References
8 Acute Myeloid Leukemia
Acute Myelogenous Leukemia
Laboratory Findings
Acute Myeloid Leukemia
with Minimal Differentiation (FAB Mo)
Acute Myeloid Leukemia without Maturation (FAB M1)
Acute Myeloid Leukemia with Maturation (FABM2)
Acute Promyelocytic Leukemia (FAB M3)
Acute Myelomonocytic Leukemia (FAB M4)
Acute Monoblastic Leukemia (M5)
Acute Erythroleukemia (M6)
Acute Megakaryoblastic Leukemia (M7)
Acute Basophilic Leukemia
Minimal Residual Disease
Therapy-Related Acute Leukemia
Congenital Leukemia
Recurrent Chromosomal Abnormalities
Acute Leukemia of Ambiguous Lineage
References
9 Acute Lymphoblastic Leukemia and Lymphoma
Acute Lymphocytic Leukemia/ Lymphoblastic Lymphoma
Laboratory Findings
Minimal Residual Disease
Lymphomas
Non-Hodgkin Lymphomas
Large-Cell Lymphomas
Anaplastic Large-Cell Lymphoma
Laboratory Findings
Hodgkin Lymphoma
Laboratory Findings
References
10 Anemias
Microcytic Anemias
Iron Deficiency Anemia
Laboratory Findings
Macrocytic Anemias
B12 and Folk Deficiency
Laboratory Findings
Normocytic Anemias
Hemolytic Anemias
Hereditary Hemolytic Anemias
Red Blood Cell Membrane Disorders
Hereditary Spherocytosis
Laboratory Findings
Hereditary Elliptocytosis Syndromes
Laboratory Findings
Other Inherited Disorders of the Red-Cell Membrane
Hereditary Anemias Due to Hemoglobin Abnormalities
Sickle Cell Anemia
Laboratory Findings
Thalassemia Syndromes
?-Thalassemias
Laboratory Findings
?-Thalassemias
Acquired Hemolytic Anemia
Hemolytic Disease of Newborn
Laboratory Findings
Autoimmune Hemolytic Anemia
Laboratory Findings
Acquired Non-Immune Hemolytic Anemias
Paroxysmal Nocturnal Hemoglobinuria
Transient Erythroblastopenia of Childhood
Aplastic Anemia
Laboratory Findings
References.
ISBN 978-3-642-62296-0
Artikelnummer 9783642622960
Medientyp Buch
Auflage Softcover reprint of the original 1st ed. 2004
Copyrightjahr 2012
Verlag Springer, Berlin
Umfang XII, 296 Seiten
Abbildungen XII, 296 p.
Sprache Englisch